Ihe kachasị sie ike ịgwọ bụ ọrịa ndị e ketara eketa bụ ndị jikọtara mkpụrụ ndụ. Ụdị ọrịa ndị a gụnyere cystic fibrosis, nke nwere ọtụtụ ebe sara mbara ma bụrụ usoro ndụ ogologo oge. E nwere ọtụtụ ụdị ọrịa a, a na-ekewa ha dịka mpaghara ahụ na njedebe nke akụkụ ahụ.
Kedu ihe bụ cystic fibrosis ma ọ bụ cystic fibrosis?
Ọrịa a kọwara bụ mmụgharị nke gene ọrụ CFTR maka maka absorption nke salts. N'ihi mgbanwe ndị na-agbanwe agbanwe, a na-ezobe nzuzo, nke dị iche iche na-emepụta n'ahụ. N'ihi oke nnu nke nnu na mkpụrụ ndụ, nakwa na enweghi mmiri, excretion nke imi siri ike, ọ na-adịgidekwa na ya, na-egbu ha. Mgbe oge na-aga na saịtị nke "nsogbu azụmahịa" a na-emepụta cysts.
Enwere 3 ụdị isi nke cystic fibrosis:
- nkwụsị;
- nsia;
- agwakọta.
E nwere mpaghara ndị ọzọ na-emetụta ọrịa, dịka ọmụmaatụ, e nwere cystic fibrosis nke lacteal na pancreas, paranasal sinuses. A naghị ahụkarị ha, ma ọ dịghị ihe dị ize ndụ karịa ụdị ụdị ọrịa a.
Mgbaàmà nke cystic fibrosis
Mgbaàmà nke cystic fibrosis dabere na mpaghara ọnya na ọdịdị nke ọrịa ahụ, yana oke ogo ya.
E gosipụtara Cystic fibrosis nke ngụgụ dị ka ndị a:
- Mwakpo ugboro ugboro nke ụkwara na-egbu mgbu;
- ọ na - esiri ike ịkewapụta sputum;
- mkpụmkpụ nke ume;
- ọganihu na-aga n'ihu;
- ogologo oyi baa;
- mmepe nke emphysema .
A na-eji ọgwụ mgbawa nke cystic fibrosis na-esonyere na mgbaàmà ndị a:
- mmegharị ụba;
- nkwonkwo ugboro;
- nkwụsịtụ ;
- oké ihe mgbu na mpaghara mgbu;
- mmepe nke usoro mmechi.
Ọtụtụ mgbe, site na ụdị cystic fibrosis, imeju na-emetụta. Nke a bụ n'ihi mmebi nke absorption na excretion nke bile na eriri afọ, nke ọ na-esi na ya pụta, na-akpali akpali
Ụdị kasị njọ nke cystic fibrosis bụ agwakọta. Ọ na-ejikọta ihe mgbaàmà nke bronchopulmonary na digestive pathology n'otu oge.
Ọgwụgwọ nke cystic fibrosis ma ọ bụ cystic fibrosis
Ọ gaghị ekwe omume ikpochapụ ọrịa ahụ a kọwara na ọrịa ruo mgbe ebighị ebi, Otú ọ dị, yana ọgwụgwọ ziri ezi kwesịrị ekwesị, àgwà ndụ nke onye nwere cystic fibrosis dị mma.
Na mgbakwunye na ọgwụ ndị dọkịta kwuru, onye ọrịa kwesịrị ịhazi ihe oriri na-edozi ahụ, na-emechi ahụike pụrụ iche, mmega ahụike iku ume.